Mandible / maxilla – Benign tumors / tumor-like conditions: juvenile ossifying fibroma. Juvenile ossifying fibroma is a rare, benign fibro-osseous tumour. In the light of a clinical case, the authors review the diagnosis, treatment and histological. Introduction. Juvenile ossifying fibroma is a rare benign fibro-osseous lesion. It is characterized by the early age of onset, the localization of the tumor, the.

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There has been so much confusion about the terminology of fibro-osseous tumors. This article has been cited by other articles in PMC. The swelling appeared normal in colour with no surface changes.

Both genders are affected equally, with ossifyng paranasal sinuses most commonly affected. Arch Pathol Lab Med. Incisional biopsy was done, and the histopathologic analysis confirmed a diagnosis of juvenile aggressive ossifying fibroma of the trabecular variety [ Figure 3 ].

Radiolucent lesion in the right maxilla.

oossifying Epub Sep Please introduce links to this page from related articles ; try the Find link tool for suggestions. Paediatric fibro-osseous lesions of the nose and paranasal sinuses.

JOAF may present as one of two histologic variants: A clinical assessment of Burkitt’s lymphoma was made, and the child was subjected to several courses of chemotherapy without adequate histologic confirmation. The tumour is well circumscribed by a tiny sclerotic shell of bone.

The nasal lesion was found to be in isolation from the maxillary lesion and was excised, labeled separately, and sent for histopathologic diagnosis. The lesion in many instances is confused with ossifying fibroma OF. A hemi-maxillectomy was planned. Juvenile aggressive ossifying fibroma is a rare clinical entity often misdiagnosed and mismanaged because of its rapidly progressive and osteolytic nature.

Within this stroma, are numerous small, rounded, mineralized collagenous ossicles and immature osteoid.


In our case, there was a well-defined radiographic margin which favoured a diagnosis of juvenile ossifying fibroma, unlike fibrous dysplasia which blends ossiying surrounding bone [ 12 ].

Most patients are asymptomatic, and come to clinical attention when a mass is discovered incidentally on routine dental X-rays. Results Because of large size of mandibular tumour, resultant expansion and destruction of mandibular cortex, the patient underwent right hemimandibulectomy using transmandibular approach. The most commonly affected facial bone is the maxilla, with facial asymmetry being the chief complaint.

Psammomatoid JOF occurs predominantly in the sinonasal and orbital bones, and trabecular JOF predominantly affects the jaws. Juvenile trabecular ossifying fibroma occurs in young patients with peaks occurring in ossigying who are below 15 years of age and is usually characterized by rapid growth and a high tendency for recurrence. Fibrous dysplasia was considered in differential diagnosis. Introduction Juvenile aggressive ossifying fibroma JAOF is a rare benign osifying locally aggressive tumor with high recurrent potentials.

Fibrous dysplasia FD is a condition characterized by excessive proliferation of bone forming mesenchymal cells which can affect one bone monostotic type or multiple bones polyostotic type. A 7-years-old female child presented to the pediatric unit of our institution with a 9-month history of right maxillary tumor. Large radiolucent area on right side of molar. Later, a compendious classification was suggested by Eversole et al.

Classical ossifying fibroma, psammomatoid juvenile ossifying fibroma, and trabecular juvenile ossifying fibroma.

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A medically fit nine-year-old male patient visited our dental department with a chief complaint of a swelling in relation to the right upper back tooth region since 3 months which was initially small jhvenile size but gradually grew up to the present size. A clinic-pathologic study of sixty-four cases. The lesion was excised along the line of cleavage. Orthopantomograph showing mixed radiolucent— radiopaque lesion in the left mandibular premolar— molar region, with flecks of calcification, displaced 35 tooth bud, with downward bowing and thining of the inferior border of the mandible Click here to view.


So taking into account the clinical, radiological, and histopathological examination, a final diagnosis of Monostotic Fibrous dysplasia in relation to the right maxillary posterior region was given.

FD affects the maxilla more than mandible and the frequent site of occurrence is the posterior region. Please review our privacy policy. Thompson; Bruce M Wenig Int J Pediatr Otorhinolaryngol. The right nostril was completely obstructed by an exophytic growth, and thus patient had to breathe via the left side [ Figure 1 ].

Case Reports in Dentistry

Histopathological features include irregular trabeculae of woven bone, blending into the surrounding normal bone that lies within a cellular fibrous stroma. The copyright, license information and link to the original publication on http: She also felt a pain and inflammation in this area.

Only curative surgical recontouring was performed in our case and patient is being recalled to check for recurrence. Males and females are equally affected [ 11 ].

Pathology Outlines – Benign tumors / tumor-like conditions: juvenile ossifying fibroma

This causes abnormal differentiation of osteoblasts and production of dysplastic bone [ 9 ]. JOAF is a distinct clinical entity, often confused with malignant conditions because of its rapidly progressive and osteolytic nature. JOAF is treated by surgical excision and may recur if local resection is not complete. Bones which bear the brunt are femur, tibia, ribs, and facial bones.