Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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Mechanisms of idiopathic constipation: Between July and June27 children were identified with HD. The Congenital Megacolon presents agonglionosis in different lengths of the intestine; many times associated to other congenital anomalies.

Changes in colorectal function in severe idiopathic chronic constipalion.

Enfermedad de Hirschsprung

The aetiology of the persistent bowel dysfunction in these patients remains controversial, but is noted to improve with age, in particular fecal incontinence 4. With respect to Somme’s 8 finding of using a rectal suction biopsy as a factor contributing to earlier diagnosis, we note the delay in diagnosis of some of the children who presented in the neonatal period Table 4.

None of the children in this series had a primary pull-through procedure. Prediction of the outcome of pull-through surgery for Hirschsprung’s disease using acetylcholinesterase activity. Hirschsprung disease in the newborn. Hirschsprung disease is certainly diagnosed after birth. An analysis of patients. The clinical presentation changes between children and adults.

It is a known fact that the clinical features of NEC – foul-smelling, explosive diarrhoea, often bloody in nature, abdominal distention, hypovolaemic shock, vomiting, fever and lethargy may mimic that of Hirschsprung’s enterocolitis. In addition, as evident in this study, a significant number of children were diagnosed with HD outside the neonatal period, and by the time of referral have well-established megarectum or megacolon, which are contraindications to the primary pullthrough procedure 9.


It should be noted however that the depicted transition zone on the contrast enema is not accurate at determining the transition between absent and present ganglion cells. Somme S, Langer JC. Hirschsprung Disease HD or Congenital Megacolon is an anomaly that is characterized mainly for the absence of ganglion cells in the myenteric plexus and submucosal in a variable segment of the intestine.

Case 4 Case 4. Loading Stack – 0 images remaining. False-positive intra-operative frozen sections reported in centres where experienced pathologists are unavailable can have serious consequences These latter children had the following procedures: Idiopathic Disorders of fecal continence in children.

Enfermedad de Hirschsprung | Neurology Associates of Kansas

The affected segment is of small caliber with proximal dilatation. Progress in management and diagnostics. A new variant of colonic ganglion cell disorders. But how safe and feasible are these newer techniques for developing countries like the Caribbean?

These include the limited number of paediatric surgical specialists and support staff and lack of facilities and equipment for the handling of frozen section specimens as well hiirschsprung paediatric pathologists trained to read and interpret frozen section specimens.

Our institution had one experience of having had a patient as outlined above who had a total colectomy and Soave pull-through procedure for presumed total colonic HD based on frozen section analysis which was later not substantiated on paraffin section.

A comparison of the nervous control of ganglionic and aganglionic smoth muscIe in vitro. A very small number may present in the adult population 1. All patients with Hirschsprung’s disease HD who had definitive surgery at the said institution over a year period between July and June were identified from hospital records.

There is ample evidence that the primary pull-through procedure for HD is safe and effective in most situations, including the neonatal period 8. Synonyms or Alternate Spellings: Case 2 Case 2. Ohservations in the inmunocytes ano macrophages in megacolon. The mean age at presentation was 30 months ranging from entermedad 1 of life to 24 years. Diagnosis of congenital megacolon: Times of first void and first stool in newborns.


The majority of children presented in hirschspprung neonatal period 10the rest being referred during infancy 7childhood 8 and adulthood 1. Medicina12 1 EnBretano, informa casos similares. Constipation is a common problem in children throughout the world, and the Caribbean is no exception. Long term outcome was assessed by the use of a simple questionnaire which was completed by the authors after personal or telephone contact with patients, their parents or guardians or the referring physician.

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Data from patients’ notes were collected to establish demographics, including age at referral and at definitive surgery, gender, presenting symptoms, presence of any associated anomalies, family history, surgical intervention s and definitive procedure.

To assess the surgical outcome of patients with Hirschsprung’s disease HD who were treated in Barbados, establish referral patterns and identify factors which can lead to better management.

Laparoscopic-assisted approaches for the definitive surgery for Hirschsprung’s disease. Gastrointestinal function after surgical correction of Hirschsprung’s Disease: Data from patients notes were collected to establish demographics, including age at referral and definitive surgery, gender, presenting symptoms, surgical intervention s and definitive procedure.